The vasculitic diseases are usually classified according to the predominant size of vessel involved.

Vasculitis by size of arteries

Detailed information on the individual vasculitides can be found under Individual Diseases

Vasculitis mainly affecting large arteries

  • Giant Cell Arteritis/Temporal Arteritis (GCA)
  • Polymyalgia Rheumatica (PMR)
  • Takayasu Arteritis (TA)

Vasculitis mainly affecting middle sized arteries

  • Polyarteritis Nodosa (PAN)
  • Kawasaki Disease (KD

Diseases affecting the small blood vessels

ANCA associated vasculitis

  • Churg Strauss Syndrome (CSS) now renamed: Eosinophillic Granulomatosis with Polyangiitis (EGPA)
  • Microscopic Polyangiitis (MPA)
  • Wegener’s Granulomatosis (WG) now renamed: Granulomatosis with Polyangiitis (GPA)

Non-ANCA vasculitis

  • Henoch-Schönlein Purpura (HSP)

Less common vasculitides

  • Behçet’s Disease (BD)
  • Buerger’s Disease
  • Central Nervous System Vasculitis (CNS)/Primary Angiitis of the Central Nervous System (PACNS)
  • Cogan’s Syndrome
  • Cryoglobulinemia and Cryoglobulinaemic Vasculitis
  • Hypersensitivity Vasculitis (HSV)
  • Rheumatoid Arthritis (RA) (secondary vasculitis)

Further reading

An excellent video that explains very clearly and graphically, the different types of vasculitis by the size of the blood vessels involved, from the Khan Academy in the USA. Khan Academy.